Dental treatment of children with krabbe syndrome with tracheostomy - Clinical case report

Abstract

People with special needs, have momentary or permanent limitations, one or more barriers, with physical, motor, cognitive, mental or sensory biological etiology. Dentistry for patients with special needs is the only specialty that works with all ages and is present in the three strands of dental care at home, outpatient and hospital allowed by the federal council. Krabbe Syndrome is an autosomal recessive neurodegenerative disease resulting from a deficiency of the enzyme galactosylceramidase, affecting the demyelination of the central and peripheral nervous system. In the literature, there are no reports on outpatient dental care for people with tracheostomy or Krabbe's disease. Given this, the objective of this study is to monitor and treat the oral health of a child with a rare syndrome with tracheostomy, who can have good oral health free of caries and periodontal disease. Thus, bringing the benefit of accessibility to outpatient dental care for children with tracheostomy, avoiding hospital interventions.